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双腔右心室:综述。

Double-chambered right ventricle: a review.

机构信息

Department of Anatomical Sciences, School of Medicine, St George's University, Grenada, West Indies.

出版信息

Cardiovasc Pathol. 2013 Nov-Dec;22(6):417-23. doi: 10.1016/j.carpath.2013.03.004. Epub 2013 May 20.

DOI:10.1016/j.carpath.2013.03.004
PMID:23701985
Abstract

A double-chambered right ventricle is a rare heart defect in which the right ventricle is separated into a high-pressure proximal and low-pressure distal chamber. This defect is considered to be congenital and typically presents in infancy or childhood but has been reported to present rarely in adults. It can be caused by the presence of anomalous muscle tissue, hypertrophy of the endogenous trabecular bands, or an aberrant moderator band; all of which will typically result in progressive obstruction of the outflow tract. In this paper, we will discuss the general anatomy of the right ventricle, the relevant embryology of the heart, and the presentation, diagnosis, and treatment of a double-chambered right ventricle.

摘要

右心室双腔是一种罕见的心脏缺陷,其中右心室分为高压近端和低压远端腔。这种缺陷被认为是先天性的,通常在婴儿期或儿童期出现,但也有罕见的成人病例报告。它可能由异常肌肉组织、内源性小梁带的肥大或异常节制带引起;所有这些都会导致流出道的进行性阻塞。本文将讨论右心室的一般解剖结构、心脏的相关胚胎学以及右心室双腔的表现、诊断和治疗。

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