Sharma Arunav, Sable Mukund N, Singla Raghav, Dash Chinmaya, Sahu Rabi Narayan
Department of Neurosurgery, AIIMS, Bhubaneswar, Odisha, India.
Department of Pathology, AIIMS, Bhubaneswar, Odisha, India.
Neurol India. 2020 Nov-Dec;68(6):1465-1468. doi: 10.4103/0028-3886.304127.
A 4-year-old male child presented with features of raised intracranial pressure due to tumor in the left lateral ventricle with shunt blockage. Ventriculoperitoneal shunt was done earlier (one month ago). Craniotomy and gross total excision of the tumor was achieved. Histopathological examination was suggestive of Atypical Teratoid/Rhabdoid tumor. Patient relatives were not compliant with the advice for adjuvant therapy and patient expired after three months of definitive surgery due to aggressive course of the disease. To the best of our knowledge only six cases of AT/RT of the lateral ventricle in pediatric population has been described in literature. The tumor may mimic radiologically with benign pathology and can have an aggressive course with poor outcome. Differential diagnosis of AT/RT must be kept in cases of lateral ventricle tumor in pediatric population.
一名4岁男童因左侧脑室肿瘤伴分流阻塞出现颅内压升高的症状。脑室腹腔分流术已于较早前（一个月前）进行。成功实施了开颅手术并将肿瘤完整切除。组织病理学检查提示为非典型畸胎样/横纹肌样瘤。患者家属未听从辅助治疗的建议，患者在确定性手术后三个月因病情进展而死亡。据我们所知，文献中仅描述了6例儿童侧脑室非典型畸胎样/横纹肌样瘤病例。该肿瘤在影像学上可能类似良性病变，且病情进展迅速，预后不良。对于儿童侧脑室肿瘤病例，必须考虑非典型畸胎样/横纹肌样瘤的鉴别诊断。
