Department of Neurosurgery, Postgraduate Institute of Medical Education & Research (PGIMER), Chandigarh, India.
Department of Neurosurgery, Postgraduate Institute of Medical Education & Research (PGIMER), Chandigarh, India,
Pediatr Neurosurg. 2020;55(6):404-408. doi: 10.1159/000511995. Epub 2020 Dec 10.
Atypical teratoid rhabdoid tumors (ATRT), an uncommon malignant intracranial tumor with aggressive behavior are mostly seen in posterior fossa in young pediatric age-group.
We present an infrequent location of this tumor in the pineal region in a 5-month-old infant. Also, the lesion was non-enhancing which was highly atypical of an ATRT. It was near-totally excised with the child placed in sitting position. However, within a short interval, a tumor recurrence was noted.
The case possibly represents an extended spectrum of congenital childhood brain tumors. Importantly, it highlights an atypical imaging of ATRT in very young children.
非典型畸胎样/横纹肌样瘤（ATRT）是一种罕见的颅内恶性肿瘤，具有侵袭性，多见于年轻的儿童后颅窝。
我们报告了一例罕见的发生于 5 月龄婴儿的松果体部位的 ATRT。此外，病变无强化，这与 ATRT 非常不典型。肿瘤在患儿取坐位时几乎完全切除。然而，在短时间内，肿瘤复发。
该病例可能代表了先天性儿童脑肿瘤的扩展谱。重要的是，它强调了非常年幼的儿童中 ATRT 不典型的影像学表现。
