Huber René, Augsten Sandra, Kirsten Holger, Zell Roland, Stelzner Axel, Thude Hansjörg, Eidner Thorsten, Stuhlmüller Bruno, Ahnert Peter, Kinne Raimund W
Experimental Rheumatology Unit, Department of Orthopedics, Jena University Hospital, Waldkliniken Eisenberg GmbH, 07607 Eisenberg, Germany.
Institute of Clinical Chemistry, Hannover Medical School, 30625 Hannover, Germany.
Life (Basel). 2020 Dec 23;11(1):5. doi: 10.3390/life11010005.
In rheumatoid arthritis (RA), the expression of many pro-destructive/pro-inflammatory proteins depends on the transcription factor AP-1. Therefore, our aim was to analyze the presence and functional relevance of mutations in the coding regions of the AP-1 subunits of the fos and jun family in peripheral blood (PB) and synovial membranes (SM) of RA and osteoarthritis patients (OA, disease control), as well as normal controls (NC). Using the non-isotopic RNAse cleavage assay, one known polymorphism (T252C: silent; rs1046117; present in RA, OA, and NC) and three novel germline mutations of the cfos gene were detected: (i) C361G/A367G: Gln121Glu/Ile123Val, denoted as "fos121/123"; present only in one OA sample; (ii) G374A: Arg125Lys, "fos125"; and (iii) C217A/G374A: Leu73Met/Arg125Lys, "fos73/125", the latter two exclusively present in RA. In addition, three novel somatic cjun mutations (604-606ΔCAG: ΔGln202, "jun202"; C706T: Pro236Ser, "jun236"; G750A: silent) were found exclusively in the RA SM. Tansgenic expression of fos125 and fos73/125 mutants in NIH-3T3 cells induced an activation of reporter constructs containing either the MMP-1 (matrix metalloproteinase) promoter (3- and 4-fold, respectively) or a pentameric AP-1 site (approximately 5-fold). Combined expression of these two cfos mutants with cjun wildtype or mutants (jun202, jun236) further enhanced reporter expression of the pentameric AP-1 construct. Finally, genotyping for the novel functionally relevant germline mutations in 298 RA, 288 OA, and 484 NC samples revealed no association with RA. Thus, functional cfos/cjun mutants may contribute to local joint inflammation/destruction in selected patients with RA by altering the transactivation capacity of AP-1 complexes.
在类风湿关节炎(RA)中,许多促破坏/促炎蛋白的表达依赖于转录因子AP-1。因此,我们的目的是分析RA和骨关节炎患者(OA,疾病对照)以及正常对照(NC)的外周血(PB)和滑膜(SM)中fos和jun家族AP-1亚基编码区突变的存在情况及其功能相关性。使用非同位素RNA酶切割分析,检测到一个已知的多态性(T252C:沉默;rs1046117;存在于RA、OA和NC中)以及cfos基因的三个新的种系突变:(i)C361G/A367G:Gln121Glu/Ile123Val,记为“fos121/123”;仅在一个OA样本中出现;(ii)G374A:Arg125Lys,“fos125”;以及(iii)C217A/G374A:Leu73Met/Arg125Lys,“fos73/125”,后两个仅在RA中出现。此外,在RA的滑膜中仅发现了三个新的体细胞cjun突变(604 - 606ΔCAG:ΔGln202,“jun202”;C706T:Pro236Ser,“jun236”;G750A:沉默)。fos125和fos73/125突变体在NIH - 3T3细胞中的转基因表达诱导了含有MMP - 1(基质金属蛋白酶)启动子(分别为3倍和4倍)或五聚体AP - 1位点(约5倍)的报告基因构建体的激活。这两个cfos突变体与cjun野生型或突变体(jun202、jun236)的联合表达进一步增强了五聚体AP - 1构建体的报告基因表达。最后,对298例RA、288例OA和484例NC样本中与功能相关的新种系突变进行基因分型,结果显示与RA无关联。因此,功能性cfos/cjun突变体可能通过改变AP - 1复合物的反式激活能力,导致部分RA患者出现局部关节炎症/破坏。