一例附着于阑尾和结肠壁的巨大肠系膜纤维瘤病，病例报告。
A giant mesenteric fibromatosis adherent to the appendix and colonic wall, case report.
作者信息
El-Helou Etienne, Alimoradi Mersad, Sabra Hassan, Naccour Jessica, Zaarour Mariana, Haddad Marwan M, Bitar Henri
机构信息
General Surgery Department, Faculty of Medical Sciences, Lebanese University, Mount Lebanon, Lebanon.
Emergency Medicine Department, Faculty of Medical Sciences, Lebanese University, Mount Lebanon, Lebanon.
出版信息
Int J Surg Case Rep. 2020;77:638-642. doi: 10.1016/j.ijscr.2020.11.109. Epub 2020 Nov 21.
BACKGROUND
Mesenteric fibromatosis, is a rare neoplasm arising usually from the bowel mesentery, with intermediate behavior and local invasion potential. They can be sporadic or related to multiple factors contributions. They usually presents as an asymptomatic growth of intraabdominal mass, and can reach a large diameter before symptoms appearance. Surgical excision is the definitive treatment when achievable.
CASE PRESENTATION
In this case we present a case of 34 years old gentleman, presenting for painless abdominal distension, and found to have a giant mesenteric fibromatosis of 23 cm diameter and 4.5 kg arising from the appendix and colonic mesentery. Treated surgically, and was free of recurrence after 1 year follow up.
CONCLUSION
We report this rare case to encourage physicians to keep this etiology in mind as part of the differential diagnosis of unspecific abdominal mass.
背景
肠系膜纤维瘤病是一种罕见的肿瘤，通常起源于肠系膜，具有中间型生物学行为和局部侵袭潜能。其可呈散发性或与多种因素有关。通常表现为腹腔内肿块的无症状性生长，在出现症状前可长得很大。若能实现，手术切除是确定性治疗方法。
病例介绍
在此病例中，我们呈现一名34岁男性患者，因无痛性腹胀就诊，发现患有一个直径23厘米、重达4.5千克的巨大肠系膜纤维瘤病，起源于阑尾和结肠系膜。接受了手术治疗，随访1年后无复发。
结论
我们报告此罕见病例，以促使医生在对非特异性腹部肿块进行鉴别诊断时将这种病因考虑在内。
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