Stoidis Christos N, Spyropoulos Basileios G, Misiakos Evangelos P, Fountzilas Christos K, Paraskeva Panorea P, Fotiadis Constantine I
Department of Surgery, Athens Navy Hospital, 70 Deinokratous Street, 11521, Athens, Greece.
J Med Case Rep. 2010 Sep 23;4:314. doi: 10.1186/1752-1947-4-314.
Intra-abdominal fibromatosis, usually located at the mesenteric level, is a locally invasive tumor of fibrous origin, with no ability to metastasize, but a tendency to recur. Certain non-typical cases of intra-abdominal fibromatosis with involvement of the bowel wall can be misdiagnosed because of their different biological behavior.
We describe the case of a 64-year-old Caucasian man presenting with mesenteric fibromatosis and involvement of the bowel wall, who was treated surgically. The macroscopic and microscopic appearance of the lesion mimicked a gastrointestinal stromal tumor, a tumor with potential malignant behavior.
It is essential to make an early and correct diagnosis in such equivocal cases, so that the appropriate treatment can be chosen and suitable patients admitted to clinical trials if appropriate. New and reliable criteria for discriminating between intra-abdominal fibromatosis and gastrointestinal stromal tumor should be proposed and established because novel sophisticated therapeutic strategies have been introduced in the international literature.
腹内纤维瘤病通常位于肠系膜层面,是一种起源于纤维组织的局部侵袭性肿瘤,无转移能力,但有复发倾向。某些累及肠壁的非典型腹内纤维瘤病病例因其不同的生物学行为可能会被误诊。
我们描述了一名64岁白种男性患者,患有肠系膜纤维瘤病并累及肠壁,接受了手术治疗。病变的宏观和微观表现类似胃肠道间质瘤,一种具有潜在恶性行为的肿瘤。
在这类模棱两可的病例中尽早做出正确诊断至关重要,以便选择合适的治疗方法,并在适当时让合适的患者参加临床试验。由于国际文献中已引入了新的复杂治疗策略,因此应提出并建立区分腹内纤维瘤病和胃肠道间质瘤的新的可靠标准。