Ahmad Hira, Halleran Devin R, Quintanilla Raquel, Gasior Alessandra C, Wood Richard J, Levitt Marc A
Department of Pediatric Colorectal and Pelvic Reconstructive Surgery, Nationwide Children's Hospital, Columbus, Ohio, United States.
European J Pediatr Surg Rep. 2020 Jan;8(1):e95-e98. doi: 10.1055/s-0040-1717128. Epub 2021 Jan 9.
Hirschsprung disease is the most common neurocristopathy in children, resulting in the congenital loss of enteric ganglia. Surgery, which involves resecting the aganglionic segment and restoring bowel continuity, usually results in a good outcome; however, some patients suffer from multiple episodes of enterocolitis and other obstructive symptoms. A contrast enema, examination under anesthesia, and rectal biopsy can identify the cause of obstruction in many cases, including a rare explanation, a twist of the pull-through, a case of which we present here.
先天性巨结肠是儿童最常见的神经嵴病,导致肠神经节先天性缺失。手术包括切除无神经节段并恢复肠道连续性,通常效果良好;然而,一些患者会多次发生小肠结肠炎和其他梗阻症状。在许多情况下,钡剂灌肠、麻醉下检查和直肠活检可以确定梗阻原因,包括一种罕见的情况,即拖出肠管扭转,我们在此介绍一例。