Morishita T, Yamazaki J, Ohsawa H, Uchi T, Kawamura Y, Okuzumi K, Nakano H, Wakakura M, Okamoto K, Koyama N
1st Department of Internal Medicine, Toho University School of Medicine, Tokyo, Japan.
Clin Cardiol. 1988 Feb;11(2):126-30. doi: 10.1002/clc.4960110213.
Primary cardiac tumor is an extremely rare disease entity. Only three cases of primary malignant cardiac schwannoma, the subject of this report, have been recorded in Japan. Recently, we encountered a case of malignant schwannoma in which retention of pericardial effusion was the first clinical finding. This case was a 30-year-old female, who had dyspnea at work, general fatigue, and fever. Striking cardiac expansion was seen, with a cardiothoracic ratio (CTR) of 69% on chest x-ray. Two-dimensional echocardiograms showed a large volume of pericardial effusion between the side wall of the left ventricle and the epicardium, and the presence of a parenchymatous tumor. An increase in tumor size was detected on chest computer tomography (CT) scan. Using a pump oxygenator, median sternotomy was performed to reach the epicardium. A pale yellow, soft tumor was seen in the left atrium near the left ventricle. Histologically, the patient was diagnosed as having a malignant schwannoma. We have reported a case of primary malignant schwannoma which was surmised to have arisen from the boundary between the atrium and the ventricle.
原发性心脏肿瘤是一种极其罕见的疾病实体。在日本,仅有三例原发性恶性心脏神经鞘瘤的记录,也就是本报告的主题。最近,我们遇到了一例以心包积液潴留为首发临床症状的恶性神经鞘瘤病例。该病例为一名30岁女性,工作时出现呼吸困难、全身乏力和发热症状。胸部X线显示心脏显著增大,心胸比率(CTR)为69%。二维超声心动图显示左心室侧壁与心外膜之间有大量心包积液,且存在实质性肿瘤。胸部计算机断层扫描(CT)显示肿瘤大小增加。使用体外循环氧合器,行正中胸骨切开术以到达心外膜。在左心房靠近左心室处可见一个淡黄色、质地柔软的肿瘤。组织学检查诊断该患者患有恶性神经鞘瘤。我们报告了一例推测起源于心房与心室交界处的原发性恶性神经鞘瘤病例。