Department of Radiology, Chung-Ang University Hospital, Chung-Ang University College of Medicine, Seoul, Korea.
Curr Med Imaging. 2022;18(1):78-81. doi: 10.2174/1573405617666210608151618.
Zinner syndrome is a rare congenital abnormality defined by a clinical triad of unilateral renal agenesis, ipsilateral seminal vesicle cyst, and ipsilateral ejaculatory duct obstruction.
Most patients are asymptomatic, but if the cystic dilatation of the seminal vesicle becomes significant, it can result in urinary symptoms such as dysuria and urinary retention. This rare developmental anomaly related to mesonephric duct can also present with other abnormalities.
Here, we report our experience of Zinner syndrome with bladder outlet obstruction and an ectopic ureter remnant.
Zinner 综合征是一种罕见的先天性异常,其临床三联征为单侧肾发育不全、同侧精囊囊肿和同侧射精管梗阻。
大多数患者无症状,但如果精囊囊肿明显扩张,可导致排尿困难和尿潴留等尿路症状。这种与中肾管发育相关的罕见发育异常也可能伴有其他异常。
本文报告了一例伴有膀胱出口梗阻和异位输尿管残端的 Zinner 综合征。