Manifestation of familial porphyria cutanea tarda after childbirth.
作者信息
Malina L, Lim C K
机构信息
Department of Dermatology, Faculty of Medical Hygiene, Charles University, Prague, Czechoslovakia.
出版信息
Br J Dermatol. 1988 Feb;118(2):243-5. doi: 10.1111/j.1365-2133.1988.tb01781.x.
Abstract
We report the case of a woman with hereditary porphyria cutanea tarda which manifested 3 weeks after she gave birth to her second child. The mother of the patient had also been diagnosed and treated for porphyria cutanea tarda. Reduced red cell uroporphyrinogen decarboxylase activity was found in the patient, the new-born child and the patient's mother. Normal enzyme activity was found in the patient's first child.
摘要
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