原发性子宫尤文肉瘤——病例报告。
Primary uterine Ewing sarcoma - A case report.
机构信息
Department of Obstetrics and Gynecology, Taipei Medical University Hospital, Taipei, Taiwan.
Department of Pathology, Taipei Medical University Hospital, Taipei, Taiwan.
出版信息
Taiwan J Obstet Gynecol. 2021 Jan;60(1):142-144. doi: 10.1016/j.tjog.2020.11.022.
OBJECTIVE
Ewing sarcoma is a type of neuroectodermal tumors (Ewing family of tumors-EFT) that mostly affect the bone or soft tissue. Primary uterine Ewing sarcoma is extremely rare.
CASE REPORT
We report a case of a primary uterine Ewing sarcoma in a 46-year-old patient, treated with total abdominal hysterectomy, and bilateral salpingo-oophorectomy and following adjuvant chemotherapy with 6 cycles of vincristine, doxorubicin, and cyclophosphamide, achieving complete remission for one year.
CONCLUSION
Complete resection for EFT is the first choice of treatment, regardless of their origins. Adjuvant chemotherapy or radiotherapy is mandatory if needed. Due to rarity of the disease, this report re-emphasizes the accurate diagnosis and appropriate treatment for these unusual tumor types occurred in female genital organs.
目的
尤文肉瘤是一种神经外胚层肿瘤（尤文家族肿瘤-EFT），主要影响骨骼或软组织。原发性子宫尤文肉瘤极为罕见。
病例报告
我们报告了一例 46 岁患者的原发性子宫尤文肉瘤，采用全子宫切除术、双侧输卵管卵巢切除术，并辅助以 6 个周期的长春新碱、多柔比星和环磷酰胺化疗，1 年达到完全缓解。
结论
EFT 的完全切除是首选治疗方法，无论其起源如何。如果需要，辅助化疗或放疗是强制性的。由于该疾病罕见，本报告再次强调了对女性生殖器官中发生的这些不常见肿瘤类型进行准确诊断和适当治疗的重要性。
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