Faizan Mahwish, Anwar Sadia, Iqbal Shahid, Mehmood Qaiser, Zaman Samina, Abbas Nasir, Mahmood Shahid, Ali Agha Shabbir
Department of Paediatric Haematology and Oncology, The Children's Hospital and ICH, Lahore.
Department of Paediatric Surgery, The Children's Hospital and ICH, Lahore.
J Coll Physicians Surg Pak. 2014 Mar;24 Suppl 1:S66-7.
Ewing's sarcoma, a primitive neuroectodermal tumour is a rare entity belonging to a family of neoplasms of neuroectodermal origin. These highly aggressive neoplasms primarily affect older children and young adults. They primarily involve the bones or soft tissues. A quarter of Ewing's sarcomas occur principally in the soft tissues with primary involvement of the kidney being exceptionally rare. We hereby, present a case of 6 years old girl child with primary Ewing's sarcoma of the kidney who presented with abdominal mass and posed much diagnostic challenge. The patient underwent complete surgical excision of tumour, and is being treated with aggressive adjuvant chemotherapy.
尤因肉瘤是一种原始神经外胚层肿瘤，是神经外胚层起源的肿瘤家族中的罕见实体。这些高度侵袭性肿瘤主要影响大龄儿童和年轻成年人。它们主要累及骨骼或软组织。四分之一的尤因肉瘤主要发生在软组织中，肾脏原发性受累极为罕见。在此，我们报告一例6岁女童原发性肾脏尤因肉瘤病例，该患儿以腹部肿块就诊，带来了很大的诊断挑战。患者接受了肿瘤的完整手术切除，并正在接受积极的辅助化疗。
