Division of Neurosurgery, Department of Neurosciences, University of the Philippines Manila-Philippine General Hospital, Manila, Philippines
Division of Neurosurgery, Department of Neurosciences, University of the Philippines Manila-Philippine General Hospital, Manila, Philippines.
BMJ Case Rep. 2021 Jan 27;14(1):e236479. doi: 10.1136/bcr-2020-236479.
Myoepithelial tumours are a rare form of salivary gland neoplasm, and their occurrence in the central nervous system is exceedingly rare. The authors report the case of an 18-year-old Filipino man presenting with headache and weakness, and on imaging showing an extensive parasagittal tumour at the left posterior parietal area with extracalvarial extension. There was no systemic disease. The patient underwent surgery to excise the tumour, with histopathology showing findings consistent with myoepithelioma. There was no further treatment, given the benign histology of the lesion, but there was recurrence after 8 months. Repeat surgery was done for the patient and he is for adjuvant radiotherapy. This appears to be the 10th reported case of a central nervous myoepithelioma, and the first case in the Philippines of a primary parasagittal myoepithelioma in a paediatric patient. Further information is needed to provide diagnostic and therapeutic recommendations.
肌上皮瘤是一种罕见的唾液腺肿瘤，其在中枢神经系统中的发生极为罕见。作者报告了 1 例 18 岁菲律宾男性患者，因头痛和无力就诊，影像学显示左侧顶枕区广泛矢状旁肿瘤，伴有颅外扩展。患者无系统性疾病。患者接受了手术切除肿瘤，组织病理学检查结果与肌上皮瘤一致。由于病变的良性组织学，没有进一步治疗，但 8 个月后复发。再次为患者进行了手术，目前正在接受辅助放疗。这似乎是第 10 例中枢神经系统肌上皮瘤，也是菲律宾首例儿童原发性矢状旁肌上皮瘤。需要进一步的信息来提供诊断和治疗建议。
