Vanderbilt University School of Medicine, Nashville, TN, U.S.A.
Department of Otolaryngology, Vanderbilt University Medical Center, Nashville, TN, U.S.A.
Laryngoscope. 2021 Apr;131(4):E1272-E1274. doi: 10.1002/lary.28920. Epub 2021 Jan 29.
High-riding jugular bulb (HRJB) is a rare condition not often observed in the clinical setting that occurs in 1% to 3% of cases. The jugular bulb is not present at birth, and the precise size and location likely depends on a myriad of postnatal events. This report describes the case of a male adolescent who experienced persistent conductive hearing loss (CHL) unilaterally following bilateral tympanostomy tube placement. Subsequent workup included computed tomography, which identified a very high jugular bulb eroding the posterior semicircular canal and occluding the round window niche. The patient had no hearing or vestibular symptoms aside from CHL and continues to be observed on a regular basis. HRJB is a rare disorder that has been known to erode the posterior semicircular canal, resulting in possible tinnitus, vertigo, dizziness, and/or sensorineural hearing loss. CHL has been reported in HRJB cases, although it is uncommon. HRJB may result in CHL through a third-window defect shunting hydromechanical energy away from the round window or due to middle ear blockage. Imaging is useful in ascertaining rare causes of CHL, such as HRJB. Because HRJB is not easily fixable, it is important to recognize it as a rare cause of CHL for appropriate patient counseling. Possible interventions should be tailored to the patient after careful consideration of contralateral anatomy and likely benefits. Laryngoscope, 131:E1272-E1274, 2021.
高位颈静脉球(HRJB)是一种罕见的临床情况,在 1%至 3%的病例中观察到。颈静脉球并非在出生时存在,其确切大小和位置可能取决于众多后天事件。本报告描述了一名男性青少年在双侧鼓室置管后单侧持续性传导性听力损失(CHL)的病例。随后的检查包括计算机断层扫描,发现一个非常高的颈静脉球侵蚀了后半规管并闭塞了圆窗龛。患者除了 CHL 之外没有听力或前庭症状,并且仍在定期观察中。HRJB 是一种罕见的疾病,已知会侵蚀后半规管,导致可能的耳鸣、眩晕、头晕和/或感音神经性听力损失。虽然不常见,但在 HRJB 病例中已报告 CHL。HRJB 可能通过第三窗缺陷将水力学能量从圆窗转移,或由于中耳阻塞导致 CHL。影像学对于确定 CHL 的罕见病因(如 HRJB)很有用。由于 HRJB 不易修复,因此重要的是认识到它是 CHL 的罕见原因,以便为患者提供适当的咨询。在仔细考虑对侧解剖结构和可能的益处后,应根据患者情况量身定制可能的干预措施。喉镜,131:E1272-E1274,2021。