Whelan T V, Maher J F, Kragel P, Dysart N, Dannenhoffer R, Prager L
Department of Medicine, Naval Hospital, Bethesda, MD 20814.
Am J Kidney Dis. 1988 Apr;11(4):353-6. doi: 10.1016/s0272-6386(88)80143-4.
Kimura's disease consists of lesions that appear as single or multiple red-brown papules or as subcutaneous nodules with a predilection for the head and neck region. Although it principally affects the skin and soft tissues, there is a high prevalence of associated renal disease. We report a case of nephrotic syndrome associated with Kimura's disease. Our patient is distinctive in that his disease first manifested while residing in the Western hemisphere; the renal disease was characterized as mesangial proliferative glomerulonephritis with renal impairment, and his nephrotic syndrome remitted with standard doses of prednisone.
木村病由单个或多个红棕色丘疹或皮下结节样病变组成，好发于头颈部区域。虽然该病主要累及皮肤和软组织，但合并肾脏疾病的发生率很高。我们报告一例与木村病相关的肾病综合征病例。我们的患者具有独特之处，即他的疾病首次出现在西半球；其肾脏疾病表现为系膜增生性肾小球肾炎伴肾功能损害，并且他的肾病综合征通过标准剂量的泼尼松得以缓解。
