Kassaian Seyed Ebrahim, Molavi Behnam, Abbasi Kyomars, Sadeghian Mohammad, Yazdani Shahrooz
Tehran Heart Center, Tehran University of Medical Sciences, Tehran, Iran.
Shahid Rajaei Hospital, Alborz University of Medical Sciences, Karaj, Iran.
J Tehran Heart Cent. 2020 Jul;15(3):131-135. doi: 10.18502/jthc.v15i3.4224.
Behçet's disease (BD) is a multisystem inflammatory disorder. Physicians should be alerted to the possibility of BD in a patient with a carotid artery pseudoaneurysm and no clear predisposing factor such as neck trauma or surgery. Endovascular repair of carotid pseudoaneurysms is technically feasible with excellent midterm follow-up results. Administration of immunosuppressive therapy before endovascular intervention is mandatory to reduce the chance of vascular complications accompanied by BD. A 40-year-old man presented with a painful and pulsatile neck mass with 2 episodes of transient ischemic attacks. The patient also complained of recurrent urogenital ulcers and aphthous lesions together with painful rashes. Ultrasonography and computed tomography angiography revealed 2 aneurysmal dilations in the left common carotid artery at the bifurcation level. He was referred to a rheumatologist, who made the diagnosis of BD. High-dose corticosteroids and cyclophosphamide were commenced. One week later, 2 overlapping self-expanding stent grafts were deployed. The final angiogram showed no residual endoleak, and the flow of the carotid and cerebral arteries was satisfactory. The patient was discharged with no neurological complications. Follow-up ultrasonography and computed tomography angiography 6 months later showed no endoleak, as well as significant shrinkage of the aneurysm sac.
白塞病(BD)是一种多系统炎症性疾病。对于患有颈动脉假性动脉瘤且无明确诱发因素(如颈部外伤或手术)的患者,医生应警惕白塞病的可能性。颈动脉假性动脉瘤的血管内修复在技术上是可行的,中期随访结果良好。在血管内干预前给予免疫抑制治疗对于减少白塞病伴发的血管并发症几率是必不可少的。一名40岁男性因颈部疼痛性搏动性肿块伴2次短暂性脑缺血发作就诊。患者还主诉反复出现泌尿生殖系统溃疡、口疮性病变以及疼痛性皮疹。超声检查和计算机断层血管造影显示左颈总动脉分叉处有2个动脉瘤样扩张。他被转诊给一名风湿病学家,后者诊断为白塞病。开始使用大剂量皮质类固醇和环磷酰胺。一周后,植入了2个重叠的自膨式支架移植物。最终血管造影显示无残余内漏,颈动脉和脑动脉血流满意。患者出院时无神经并发症。6个月后的随访超声检查和计算机断层血管造影显示无内漏,动脉瘤囊显著缩小。