Kassaian Seyed Ebrahim, Abbasi Kyomars, Shirzad Mahmood, Anvari Maryam Sotoudeh, Shahrzad Maryam, Molavi Behnam
Tehran Heart Center, Tehran University of Medical Sciences, Tehran, Iran.
Dr. Shariati Hospital, Tehran University of Medical Sciences, Tehran, Iran.
J Tehran Heart Cent. 2014;9(4):179-82. Epub 2014 Jul 6.
Behcet's disease is a rare immune mediated systemic vasculitis which besides it's more frequent involvement of eyes and skin, sometimes present with aortic pseudo aneurysm and more rarely cardiac inflammatory masses.A 51-year-old patient with Behçet's Disease presented with two symptomatic aortic pseudoaneurysms concomitant with a right atrial mass. Computed tomography (CT) revealed one supra-celiac and another infrarenal aortic pseudoaneurysms. Echocardiography showed a large mobile mass in the right atrium. Both pseudoaneurysms were successfully excluded simultaneously via endovascular approach with Zenith stent-grafts, and the atrial mass was surgically removed 10 days later. Post-implant CT showed successful exclusion of both pseudo-aneurysms, patency of all relevant arteries, and patient is now asymptomatic and has returned to normal lifestyle. Multiple pseudoaneurysms concomitant with a right atrial mass can be an initial manifestation of Behçet's disease. Endovascular repair can be a good treatment option for the pseudoaneurysms.
白塞病是一种罕见的免疫介导的系统性血管炎，除了更常累及眼睛和皮肤外，有时还会出现主动脉假性动脉瘤，更罕见的是心脏炎性肿块。一名51岁的白塞病患者出现了两个有症状的主动脉假性动脉瘤，同时伴有右心房肿块。计算机断层扫描（CT）显示一个腹腔干上方和另一个肾下主动脉假性动脉瘤。超声心动图显示右心房有一个大的活动肿块。两个假性动脉瘤均通过使用Zenith覆膜支架经血管内途径成功同时排除，10天后手术切除心房肿块。植入后CT显示两个假性动脉瘤均成功排除，所有相关动脉通畅，患者目前无症状，已恢复正常生活方式。伴有右心房肿块的多个假性动脉瘤可能是白塞病的初始表现。血管内修复对于假性动脉瘤可能是一个很好的治疗选择。
