Department of Pediatric Surgery, SVP Post Graduate Institute of Pediatrics, SCB Medical College, Cuttack, Odisha, India.
Afr J Paediatr Surg. 2021 Jan-Mar;18(1):33-38. doi: 10.4103/ajps.AJPS_53_20.
Congenital pouch colon (CPC) is an unusual anomaly with an unique geographical distribution. The aim of this study was to find out the incidence of CPC among anorectal malformation (ARM) cases in our institute and to compare the outcome between conventional three-staged surgery versus two-staged management approach.
This study was conducted in the department of pediatric surgery over a period of 7 years from 1 April 2013 to 31 March 2020.
Out of 754 cases of ARMs, 43 cases of CPC were detected. The incidence of pouch colon among patients with high ARMs was found to be 7.6% with a male predominance (M:F = 4.4:1). The anomaly was diagnosed in 72% of our patients preoperatively and Type IV variety was the most common intra-operative finding. The survival after initial hospitalisation was 82% and 88% in three-stage and two-stage surgical procedures, respectively. However, the final clinical outcome after the completion of all stages of surgery and follow-up was better in two-staged approach (54% vs. 47%).
Although, CPC is a rare anomaly, the incidence in our institute is 7.6% among high ARM cases. As compared to conventional three-staged surgery, the two-staged management approach has the advantage of better survival and decreased morbidity.
先天性囊状结肠（CPC）是一种罕见的异常，具有独特的地理分布。本研究旨在探讨我院肛门直肠畸形（ARM）病例中 CPC 的发生率，并比较传统的三阶段手术与两阶段治疗方法的结果。
这项研究是在 2013 年 4 月 1 日至 2020 年 3 月 31 日期间在小儿外科部门进行的，为期 7 年。
在 754 例 ARM 中，发现 43 例 CPC。高位 ARM 患者中囊状结肠的发生率为 7.6%，男性占优势（M:F=4.4:1）。72%的患者在术前被诊断出患有该疾病，且最常见的术中发现是 IV 型。初次住院后的存活率分别为三阶段手术和两阶段手术的 82%和 88%。然而，在完成所有阶段的手术和随访后，两阶段方法的最终临床结局更好（54%比 47%）。
尽管 CPC 是一种罕见的异常，但在我院高位 ARM 病例中的发生率为 7.6%。与传统的三阶段手术相比，两阶段治疗方法具有更好的生存率和降低发病率的优势。
