Nigro Raffaele, Scogna Antonio Alessandro, Intraina Daniele, Toccaceli Giada, Ieraci Alfio, Zotta Donato Carlo
Department of Emergency Neurosurgery, Pescara Hospital, Pescara, Abruzzo, Italy.
Department of Pathology, Pescara Hospital, Pescara, Abruzzo, Italy.
Surg Neurol Int. 2021 Jan 20;12:21. doi: 10.25259/SNI_878_2020. eCollection 2021.
Melanocytomas are rare pigmented tumors of the central nervous system (CNS). They are more frequent in females in their fifties and are typically benign, but locally aggressive lesions that very are rarely found in the spine. They can occur in all the age groups.
A 62-year-old male presented with acute paraplegia a attributed to a C7-T1 intradural extramedullary melanocytoma. Urgent surgery, consisting of subtotal removal of the lesion, resulted in subtotal recovery of motor function with full resolution of his sensory deficit. Histologically, the lesion proved to be a melanocytoma.
Rarely, patients with intradural extramedullary melanocytomas of the spine may present with acute paralytic deficits warranting emergent surgical intervention.
黑素细胞瘤是中枢神经系统(CNS)罕见的色素性肿瘤。多见于五十多岁的女性,通常为良性,但局部侵袭性病变在脊柱中极为罕见。可发生于所有年龄组。
一名62岁男性因C7-T1节段硬膜内髓外黑素细胞瘤出现急性截瘫。紧急手术,包括次全切除病变,导致运动功能部分恢复,感觉障碍完全消失。组织学检查显示,该病变为黑素细胞瘤。
罕见情况下,脊柱硬膜内髓外黑素细胞瘤患者可能出现急性麻痹性缺陷,需要紧急手术干预。