Farinha Nuno Cubas, Teixeira Joaquim Cruz, Reis José Hipólito, Coiteiro Domingos
Department of Neurosurgery, Centro Hospitalar Universitário Lisboa Norte EPE, Avenida Professor Egas Moniz.
Department of Neurosurgery, CUF Infante Santo Hospital, Travessa do Castro, Lisbon, Portugal.
Surg Neurol Int. 2021 Feb 10;12:53. doi: 10.25259/SNI_651_2020. eCollection 2021.
The filum terminale arteriovenous fistulas (FTAVFs) are a very rare type of spinal vascular malformation. Clinically, these lesions could present with a progressive ascending myelopathy also called FoixAlajouanine syndrome. Due to the rarity of these vascular malformation, some can be misdiagnosed, submitted to unnecessary spinal surgery, and even masqueraded as a failed back surgery syndrome. Based on the present case and related literature, we review all the cases with similar history and describe factors that should raise awareness for diagnosis of this spinal vascular malformation.
We present a case of a patient with a FTAVF at the level of L5-S1 that presented with a FoixAlajouanine syndrome. He had been previously submitted to a lumbar decompressive laminectomy without sustained improvement. After the identification and surgical treatment of the vascular malformation, he had progressive neurological improvement.
FTAVF is a very rare spinal intradural spinal vascular malformation that can be masqueraded as a failed back surgery syndrome. In these cases, signs of ascending myelopathy should prompt awareness and vascular voids must be carefully evaluated in MRI.
终丝动静脉瘘(FTAVF)是一种非常罕见的脊髓血管畸形。临床上,这些病变可表现为进行性上升性脊髓病,也称为福-阿综合征。由于这些血管畸形的罕见性,一些病例可能被误诊,接受不必要的脊柱手术,甚至被误诊为腰椎手术失败综合征。基于本病例及相关文献,我们回顾了所有具有相似病史的病例,并描述了应提高对这种脊髓血管畸形诊断意识的因素。
我们报告一例L5-S1水平的FTAVF患者,表现为福-阿综合征。他之前接受过腰椎减压椎板切除术,但病情未持续改善。在识别并手术治疗血管畸形后,他的神经功能逐渐改善。
FTAVF是一种非常罕见的脊髓硬膜内脊髓血管畸形,可被误诊为腰椎手术失败综合征。在这些病例中,上升性脊髓病的体征应引起注意,并且必须在MRI中仔细评估血管间隙。