Adnexal Service, Moorfields Eye Hospital.
Department of Eye Pathology, UCL Institute of Ophthalmology, London, United Kingdom.
Ophthalmic Plast Reconstr Surg. 2021;37(5):e164-e167. doi: 10.1097/IOP.0000000000001958.
Solitary orbital neurilemmoma-a benign tumor of Schwann cells in a peripheral nerve-sheath-are typically very slow growing and present in middle age; in the absence of neurofibromatosis, they are almost never seen in childhood. We describe the clinical presentation, imaging, pathology, and management of this tumor in a 12 years old-the tumor growing extremely rapidly over 5 months and without any evidence of cystic degeneration, hemorrhage, or sarcomatous features. The possibility of tumor growth having been accelerated by prior biopsy is discussed.
孤立性眶内神经鞘瘤——一种发生于外周神经鞘的施万细胞良性肿瘤——通常生长非常缓慢，见于中年；在无神经纤维瘤病的情况下，在儿童中几乎从未见过。我们描述了一例 12 岁患儿的临床表现、影像学表现、病理学和治疗方法，肿瘤在 5 个月内迅速生长，没有任何囊性变性、出血或肉瘤样特征的证据。讨论了先前活检加速肿瘤生长的可能性。
