Department of Pediatric Surgery, University Hospital Center, Centre Hospitalier Universitaire d'Amiens, 1, rond-point Christian Cabrol, 80054 Amiens cedex 1, France.
Department of Obstetrics and Gynecology, University Hospital Center, Centre Hospitalier Universitaire d'Amiens, 1, rond-point Christian Cabrol, 80054 Amiens cedex 1, France.
Arch Pediatr. 2021 May;28(4):345-347. doi: 10.1016/j.arcped.2021.02.003. Epub 2021 Mar 11.
Ureteropelvic junction obstruction (UPJO) in the upper pole of a complete duplicated renal system is extremely rare. We report a case that was diagnosed prenatally and we review 10 cases published in the literature. Diagnoses of adrenal hematoma and cystic neuroblastoma were suspected on prenatal ultrasound, based on the severity of dilatation and the difficulty of identifying the exact origin of this anomaly. Neonatal magnetic resonance imagery (MRI) was subsequently able to show a normal adrenal gland. Surgical management is similar to that of a single-system pyeloureteral junction obstruction. Since this situation is very rare, we believe cystoscopy can be useful to confirm diagnosis of UPJO associated with complete duplication, especially in the absence of preoperative MRI. Among the 11 surgical cases previously published, seven patients underwent pyeloplasty and four heminephrectomy.
完全重复肾系统上极肾盂输尿管连接部梗阻（UPJO）极为罕见。我们报告了 1 例产前诊断病例，并复习了文献中报道的 10 例病例。产前超声检查根据扩张的严重程度和难以确定该异常的确切起源，提示存在肾上腺血肿和囊性神经母细胞瘤的可能。随后新生儿磁共振成像（MRI）显示正常的肾上腺。手术治疗类似于单侧系统肾盂输尿管连接部梗阻。由于这种情况非常罕见，我们认为膀胱镜检查有助于确认与完全重复相关的 UPJO 诊断，特别是在没有术前 MRI 的情况下。在之前发表的 11 例手术病例中，7 例行肾盂成形术，4 例行半肾切除术。
