Ure B M, Holschneider A M, Gharib M, Halsband H, Hinselmann D
Kinderchirurgische Klinik des Kinderkrankenhauses der Stadt Köln.
Z Kinderchir. 1988 Feb;43(1):27-30. doi: 10.1055/s-2008-1043407.
Seven cases of fibromatoses in infancy and childhood serve as examples to demonstrate this group of rare tumours, taking especially the aggressive forms of juvenile fibromatoses into account. There is a tendency to locally invasive destructive growth without metastasising at any time and a markedly high relapse rate after surgery--a tendency that showed up clearly in our patients, too. Only one child out of four having infantile (desmoid-type) fibromatosis of different localisation did not show any recurrence. The article reports, among other cases, on a desmoid of the stomach and oesophagus in a 15-year-old girl, not described in the literature so far, and on a congenital fibromatosis of the pancreas. Several classifications had to be performed to properly grade the individual cases (1, 6), since no generally valid systematic description of these tumours exists.
7例婴幼儿及儿童期纤维瘤病病例可作为实例，用以展示这组罕见肿瘤，尤其考虑到青少年纤维瘤病的侵袭性形式。其具有局部侵袭性破坏性生长的倾向，且任何时候都不会发生转移，术后复发率显著较高——这种倾向在我们的患者中也明显表现出来。4例患有不同部位婴儿型（硬纤维瘤型）纤维瘤病的儿童中，只有1例未出现任何复发情况。除其他病例外，本文还报道了1例15岁女孩的胃及食管硬纤维瘤，这是迄今文献中未描述过的，以及1例胰腺先天性纤维瘤病。由于目前尚无对这些肿瘤普遍有效的系统描述，因此必须进行几种分类才能对各个病例进行恰当分级（1, 6）。
