Lee Jae Jun, Lee Ok Jeong, Yang Ji-Hyuk, Jun Tae-Gook
Department of Thoracic and Cardiovascular Surgery, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, Korea.
J Chest Surg. 2021 Oct 5;54(5):389-392. doi: 10.5090/jcs.20.105.
Double outlet right ventricle (DORV) with pulmonary atresia (PA) is an uncommon congenital disease. Because of anatomical and physiological anomalies in the systemic and pulmonary circulation, corrective surgery may be challenging. We present the case of a patient with DORV and PA. This condition was successfully corrected using a modified Nikaidoh procedure, resulting in reduced obstruction of the left ventricular outflow tract.
右心室双出口合并肺动脉闭锁是一种罕见的先天性疾病。由于体循环和肺循环存在解剖和生理异常,矫正手术可能具有挑战性。我们报告一例右心室双出口合并肺动脉闭锁患者的病例。采用改良尼凯多手术成功矫正了该病症,减轻了左心室流出道梗阻。