Orthopedics Department, Necker - Enfants Malades University Hospital, Paris.
Department of Orthopedics, Children's Hospital, CHU de Toulouse, France.
J Pediatr Orthop B. 2021 May 1;30(3):257-263. doi: 10.1097/BPB.0000000000000785.
Severe infant osteogenesis imperfecta requires osteosynthesis. Intramedullary tibia's osteosynthesis is a technical challenge given the deformity and the medullar canal's narrowness. We describe an extramedullary technique: 'In-Out-In' K-wires sliding. We performed an anteromedial diaphysis approach. The periosteum was released while preserving its posterior vascular attachments. To obtain a straight leg, we did numerous osteotomies as many times as necessary. K-wires ('In') were introduced into the proximal epiphysis, and the medial malleolus ('Out') bordered the cortical and ('In') reach their opposite metaphysis. K-wires were cut, curved and impacted at their respective epiphysis ends to allow a telescopic effect. All tibial fragments are strapped on K-wires, and the periosteum was sutured over it. Our inclusion criteria were children with osteogenesis imperfecta operated before 6 years old whose verticalization was impossible. Seven patients (11 tibias) are included (2006-2016) with a mean surgery's age of 3.3 ± 1.1 years old. All patients received intravenous bisphosphonates preoperatively. The follow-up was 6.1 ± 2.7 years. All patients could stand up with supports, and the flexion deformity correction was 46.7 ± 14.2°. Osteosynthesis was changed in nine tibias for the arrest of telescoping with flexion deformity recurrence and meantime first session-revision was 3.8 ± 1.7 years. At revision, K-wires overlap had decreased by 55 ± 23%. Including all surgeries, three distal K-wires migrations were observed, and the number of surgical procedures was 2.5/tibia. No growth arrest and other complications reported. 'In-Out-In' K-wires sliding can be considered in select cases where the absence of a medullary canal prevents the insertion of intramedullary rod or as a salvage or alternative procedure mode of fixation. It can perform in severe infant osteogenesis imperfecta under 6 years old with few complications and good survival time.
严重婴儿型成骨不全症需要进行骨科内固定。由于胫骨畸形和骨髓腔狭窄,胫骨髓内固定是一项技术挑战。我们描述了一种髓外技术:“内外进”克氏针滑动法。我们采用前内侧骨干入路。在保留其后方血管附着的情况下,切开骨膜。为了获得直腿,我们根据需要进行了多次截骨。将克氏针(“内”)插入近侧骺端,内踝(“外”)位于皮质边缘,并(“内”)到达对侧干骺端。克氏针被剪断、弯曲并打入各自的骺端,以产生伸缩效果。所有胫骨碎片都用克氏针固定,骨膜缝合在上面。我们的纳入标准是 6 岁以下接受过手术且无法垂直化的成骨不全症患儿。2006 年至 2016 年间共纳入 7 例患者(11 胫骨),平均手术年龄为 3.3 ± 1.1 岁。所有患者术前均接受静脉内双膦酸盐治疗。随访时间为 6.1 ± 2.7 年。所有患者均能在支撑下站立,且屈曲畸形矫正度为 46.7 ± 14.2°。9 例胫骨因伸缩伴屈曲畸形复发而更换内固定,同时首次翻修时间为 3.8 ± 1.7 年。翻修时,克氏针重叠减少了 55 ± 23%。包括所有手术,有 3 例远端克氏针移位,每胫骨手术次数为 2.5 次。无生长停滞和其他并发症报告。在缺乏骨髓腔妨碍髓内棒插入的情况下,或作为固定的挽救或替代方式,可以考虑采用“内外进”克氏针滑动法。该方法可用于 6 岁以下严重婴儿型成骨不全症,并发症少,存活率高。