Yolcu Alkım, Tulay Cumhur Murat, Temiz Peyker, Aydoğdu İsmet
Department of Internal Medicine, Manisa Celal Bayar University, Faculty of Medicine, Manisa, Turkey.
Department of Thoracic Surgery, Manisa Celal Bayar University, Faculty of Medicine, Manisa, Turkey.
Turk Gogus Kalp Damar Cerrahisi Derg. 2021 Jan 13;29(1):126-128. doi: 10.5606/tgkdc.dergisi.2021.19685. eCollection 2021 Jan.
Langerhans cell histiocytosis, formerly known as histiocytosis X, represents clonal proliferations of the antigen-presenting dendritic cells, which are normally found in many organs. It is a rare disease which tends to affect children and adolescents. In particular, adult-onset type is very rare. Herein, we present a female adult diagnosed with Langerhans cell histiocytosis of the rib without any systemic involvement which was successfully treated with surgery.
朗格汉斯细胞组织细胞增多症,以前称为组织细胞增多症X,是抗原呈递树突状细胞的克隆性增殖,这些细胞通常存在于许多器官中。它是一种罕见疾病,倾向于影响儿童和青少年。特别是成人发病型非常罕见。在此,我们报告一例成年女性,诊断为肋骨朗格汉斯细胞组织细胞增多症,无任何全身受累,通过手术成功治疗。