Sangeetha Geminiganesan, Dhanabal Divya, Mouttou Prebagarane Saktipriya, Janarthanan Mahesh
Pediatric Nephrology, Sri Ramachandra Institute of Higher Education and Research, Chennai, Tamilnadu, India.
Pathology, Sri Ramachandra Institute of Higher Education and Research, Chennai, Tamil Nadu, India.
BMJ Case Rep. 2021 Apr 1;14(4):e241152. doi: 10.1136/bcr-2020-241152.
Juvenile dermatomyositis (JDM) is the most common inflammatory myopathy in children and is characterised by the presence of proximal muscle weakness, heliotrope dermatitis, Gottron's papules and occasionally auto antibodies. The disease primarily affects skin and muscles, but can also affect other organs. Renal manifestations though common in autoimmune conditions like lupus are rare in JDM. We describe a child whose presenting complaint was extensive calcinosis cutis. Subtle features of proximal muscle weakness were detected on examination. MRI of thighs and a muscle biopsy confirmed myositis. Nephrocalcinosis was found during routine ultrasound screening. We report the first case of a child presenting with rare association of dermatomyositis, calcinosis cutis and bilateral medullary nephrocalcinosis.
幼年皮肌炎(JDM)是儿童中最常见的炎性肌病,其特征为近端肌无力、向阳疹、Gottron丘疹,偶尔还伴有自身抗体。该病主要影响皮肤和肌肉,但也可累及其他器官。肾脏表现虽然在狼疮等自身免疫性疾病中很常见,但在JDM中却很少见。我们描述了一名以广泛皮肤钙质沉着为主要诉求的儿童。检查时发现了近端肌无力的细微特征。大腿MRI和肌肉活检证实为肌炎。在常规超声筛查中发现了肾钙质沉着。我们报告了首例出现皮肌炎、皮肤钙质沉着和双侧髓质肾钙质沉着罕见关联的儿童病例。