Department of Cardiovascular Surgery, Faculty of Medicine, University of Tsukuba, Tsukuba, Japan.
Department of Cardiovascular Surgery, University Medical Center, University of Medicine and Pharmacy at Ho Chi Minh City, Ho Chi Minh City, Vietnam.
Heart Surg Forum. 2021 Mar 30;24(2):E333-E335. doi: 10.1532/hsf.3665.
Right ventricular myxoma is very rare, especially its originating from the right ventricular outflow tract (RVOT) and extending to the main pulmonary artery. Here, we report a case of a giant RVOT myxoma, indistinguishable from pulmonary embolism (PE). Although the myxoma is a candidate for urgent surgery, this case satisfied diagnostic criteria for PE and had no indication for intervention, according to the guideline. The strategy for this mass can be completely different, depending on the diagnosis. Surgical extraction was selected because of atypical clinical course, findings, and nagging debut for neoplasm. Then it made hemodynamic status stable by releasing RVOT obstruction and allowed to reveal the diagnosis as myxoma histopathologically.
右心室黏液瘤非常罕见,尤其是起源于右心室流出道(RVOT)并延伸至主肺动脉的黏液瘤。在此,我们报告一例巨大 RVOT 黏液瘤,与肺栓塞(PE)难以区分。尽管黏液瘤是紧急手术的候选者,但根据指南,该病例符合 PE 的诊断标准,且无介入指征。根据诊断,该肿块的治疗策略可能完全不同。由于非典型的临床过程、发现和肿瘤的初期症状,选择了手术切除。然后,通过解除 RVOT 梗阻使血流动力学状态稳定,并进行黏液瘤的组织病理学诊断。