Teran Santiago, Camara Jurado Maria, Nuñez Sobrino Juan Antonio
Medical Oncology Department, Hospital Universitario 12 de Octubre, Madrid, Spain.
Pathology Department, Hospital Universitario 12 de Octubre, Madrid, Spain.
Case Rep Oncol Med. 2021 Mar 31;2021:8896254. doi: 10.1155/2021/8896254. eCollection 2021.
Mixed neuroendocrine non-neuroendocrine neoplasms (MiNENs) are rare tumors composed of two different histological components, one of which is of a neuroendocrine origin. Given its suggested underdiagnosis and consequent low prevalence, no clear diagnostic and treatment guidelines are available, and treatment usually follows regimens similar to that of the most aggressive component. On the other hand, multiple primary tumors (MPTs) are also rare neoplastic entities that usually confer a challenge regarding treatment options, for a regimen that comprises both the primary and the synchronous/metachronous malignancy should be used. Here, we discuss the challenging diagnostic and therapeutic management of a patient with an ileocecal MiNEN that presented along with a synchronous squamous non-small-cell lung cancer (SQ-NSCLC). The patient presented with intestinal obstruction symptoms for which he underwent an emergency resection of the ileocecal MiNEN. An initial CT scan showed an additional lung mass later identified as an SQ-NSCLC after bronchoscopy biopsy analysis. Given the rapid hepatic metastatic progression, palliative platinum-based chemotherapy was initiated, with an adequate response of the local and metastatic lesions of the MiNEN, but suggested platinum resistance and progression of the pulmonary neoplasm. Second-line treatment with pembrolizumab directed for the SQ-NSCLC was initiated; however, it was stopped after immune-mediated toxicities developed. A third-line chemotherapy scheme with carboplatin/gemcitabine was initiated, but central nervous system (CNS) progression developed, with the patient dying 11 months after initial diagnosis.
混合性神经内分泌-非神经内分泌肿瘤(MiNENs)是由两种不同组织学成分组成的罕见肿瘤,其中一种起源于神经内分泌。鉴于其可能存在诊断不足及由此导致的低发病率,目前尚无明确的诊断和治疗指南,治疗通常遵循与最具侵袭性成分相似的方案。另一方面,多原发性肿瘤(MPTs)也是罕见的肿瘤实体,通常在治疗选择方面带来挑战,因为应采用包含原发性肿瘤以及同步性/异时性恶性肿瘤的治疗方案。在此,我们讨论一名患有回盲部MiNEN并伴有同步性肺鳞状非小细胞癌(SQ-NSCLC)患者具有挑战性的诊断和治疗管理情况。该患者因肠梗阻症状接受了回盲部MiNEN的急诊切除。最初的CT扫描显示肺部有一额外肿块,经支气管镜活检分析后后来确定为SQ-NSCLC。鉴于肝脏转移进展迅速,开始了以铂类为基础的姑息化疗,MiNEN的局部和转移病灶有适当反应,但提示铂类耐药且肺部肿瘤进展。针对SQ-NSCLC开始使用派姆单抗进行二线治疗;然而,在出现免疫介导的毒性反应后停药。开始了卡铂/吉西他滨的三线化疗方案,但出现了中枢神经系统(CNS)进展,患者在初次诊断后11个月死亡。