Seto H, Matsukado Y, Kuratsu J, Takaki S, Tomoda K
Department of Neurosurgery, Kumamoto University Medical School, Japan.
No Shinkei Geka. 1988 Apr;16(4):409-13.
Angiosarcoma is a rare malignant tumor originating from vascular endothelial cells. We have experienced a case of 17-year-old man, who had angiosarcoma in the pineal region and the liver. Patient's initial symptom was headache and CT scan revealed a high density mass in the pineal region with obstructive hydrocephalus. After the radiation therapy, the tumor was disappeared completely on CT scan. One year later, he developed abdominal pain, and CT scan and angiogram revealed multiple angioma like lesions in the liver. The mass in the pineal region showed concomitant regrowth, and finally, the patient was died of abdominal hemorrhage. At autopsy, pineal tumor and hepatic tumor were both angiosarcomas, although it was uncertain which was the original tumor.
血管肉瘤是一种起源于血管内皮细胞的罕见恶性肿瘤。我们遇到过一例17岁男性患者，其松果体区和肝脏患有血管肉瘤。患者最初的症状是头痛，CT扫描显示松果体区有一个高密度肿块并伴有梗阻性脑积水。放疗后，CT扫描显示肿瘤完全消失。一年后，他出现腹痛，CT扫描和血管造影显示肝脏有多个血管瘤样病变。松果体区的肿块显示有复发，最终，患者死于腹腔出血。尸检发现，松果体肿瘤和肝脏肿瘤均为血管肉瘤，尽管尚不确定哪个是原发肿瘤。
