Sana Ilenia, Mantione Maria Elena, Angelillo Piera, Muzio Marta
Division of Experimental Oncology, San Raffaele Hospital IRCCS, Milano, Italy.
Lymphoma Unit, Department of Onco-Hematology, IRCCS San Raffaele Scientific Institute, Milan, Italy.
Front Oncol. 2021 Apr 1;11:651057. doi: 10.3389/fonc.2021.651057. eCollection 2021.
In recent years significant progress has been made in the clinical management of chronic lymphocytic leukemia (CLL) as well as other B-cell malignancies; targeting proximal B-cell receptor signaling molecules such as Bruton Tyrosine Kinase (BTK) and Phosphoinositide 3-kinase (PI3Kδ) has emerged as a successful treatment strategy. Unfortunately, a proportion of patients are still not cured with available therapeutic options, thus efforts devoted to studying and identifying new potential druggable targets are warranted. B-cell receptor stimulation triggers a complex cascade of signaling events that eventually drives the activation of downstream transcription factors including Nuclear Factor of Activated T cells (NFAT). In this review, we summarize the literature on the expression and function of NFAT family members in CLL where NFAT is not only overexpressed but also constitutively activated; NFAT controls B-cell anergy and targeting this molecule using specific inhibitors impacts on CLL cell viability. Next, we extend our analysis on other mature B-cell lymphomas where a distinct pattern of expression and activation of NFAT is reported. We discuss the therapeutic potential of strategies aimed at targeting NFAT in B-cell malignancies not overlooking the fact that NFAT may play additional roles regulating the inflammatory microenvironment.
近年来,慢性淋巴细胞白血病(CLL)以及其他B细胞恶性肿瘤的临床管理取得了重大进展;靶向近端B细胞受体信号分子,如布鲁顿酪氨酸激酶(BTK)和磷酸肌醇3激酶(PI3Kδ),已成为一种成功的治疗策略。不幸的是,一部分患者仍然无法通过现有的治疗方案治愈,因此致力于研究和确定新的潜在可药物化靶点的努力是必要的。B细胞受体刺激引发一系列复杂的信号事件,最终驱动包括活化T细胞核因子(NFAT)在内的下游转录因子的激活。在这篇综述中,我们总结了关于NFAT家族成员在CLL中的表达和功能的文献,其中NFAT不仅过度表达而且持续激活;NFAT控制B细胞无能,使用特异性抑制剂靶向该分子会影响CLL细胞的活力。接下来,我们将分析扩展到其他成熟B细胞淋巴瘤,其中报道了NFAT的独特表达和激活模式。我们讨论了针对B细胞恶性肿瘤中NFAT的治疗策略的潜力,同时也不忽视NFAT可能在调节炎症微环境中发挥其他作用这一事实。