Gordon Elliott S, Wagner Lauren A, Kennedy Joanne M
Department of Pediatrics, Mercer University School of Medicine, Macon, Georgia, USA
Department of Pediatrics, Atrium Health Navicent Beverly Knight Olson Children's Hospital, Macon, Georgia, USA.
BMJ Case Rep. 2021 Apr 21;14(4):e239520. doi: 10.1136/bcr-2020-239520.
Gastroschisis is an uncommon congenital defect of the abdominal wall resulting in intestinal prolapse, most commonly associated with short gut syndrome or bowel obstruction. Wandering spleen, movement of the spleen due to the underdevelopment of splenic ligaments, has a prevalence of 0.25% and is asymptomatic in 15% of paediatric cases. An 11-year-old patient, admitted with a history of gastroschisis repaired at birth, presents with 18 months of intermittent, worsening abdominal pain. Imaging demonstrated splenomegaly and tortuosity of the splenic vein with abnormal positioning of the superior mesenteric artery and vein. The patient was found to have a wandering spleen with subacute splenic infarct secondary to splenic torsion, necessitating emergent surgical intervention. This patient experienced an extremely rare complication of gastroschisis that has not previously been reported. This complication is caused by a lack of appropriate abdominal fixation points for the spleen.
腹裂是一种罕见的腹壁先天性缺陷,可导致肠道脱垂,最常与短肠综合征或肠梗阻相关。游走脾是由于脾韧带发育不全导致脾脏移位,其患病率为0.25%,在15%的儿科病例中无症状。一名11岁患者,有出生时腹裂修补病史,因间歇性、逐渐加重的腹痛18个月入院。影像学检查显示脾肿大、脾静脉迂曲,肠系膜上动静脉位置异常。该患者被发现患有游走脾并继发脾扭转导致亚急性脾梗死,需要紧急手术干预。该患者经历了一种腹裂极其罕见的并发症,此前未见报道。这种并发症是由于脾脏缺乏合适的腹部固定点所致。