Benedetto Caterina, Barbaro Ugo, Anfuso Carmelo, Militi Annalisa, Morabito Rosa, Ruvolo Claudio, Monaco Francesco
Department of Radiology, I.R.C.C.S. Centro Neurolesi Bonino Pulejo P.O Piemonte, Viale Europa 45, 98124 Messina, Italy.
Thoracic Surgery Unit, Policlinico G. Martino, Hospital of the University of Messina, 98125 Messina, Italy.
Radiol Case Rep. 2021 Apr 2;16(6):1325-1328. doi: 10.1016/j.radcr.2021.03.004. eCollection 2021 Jun.
Lymphangioleiomyomatosis (LAM) is a rare, idiopathic, cystic disease that affects lungs of young women at childbearing age. Usually, LAM clinical manifestations are pneumothorax, progressive dyspnea and chylous pleural effusions. In many cases, due to unusual and nonspecific symptoms, LAM is mis-recognized and patients, who are affected by such disease, receive delayed diagnosis. This case report focuses on a 45-year-old woman patient with asymptomatic lymphangioleiomyomatosis who presented a big cyst which makes it looks like hydropneumothorax condition. Although chest radiograph and following CT scan has given an incidental diagnosis of right hydropneumothorax, treatment with drainages and video-assisted thorascopic surgery, instead, has allowed us to formulate correct diagnosis of cysts in LAM.
淋巴管平滑肌瘤病（LAM）是一种罕见的特发性囊性疾病，影响育龄期年轻女性的肺部。通常，LAM的临床表现为气胸、进行性呼吸困难和乳糜性胸腔积液。在许多情况下，由于症状不寻常且不具特异性，LAM被误诊，患有这种疾病的患者得到延迟诊断。本病例报告聚焦于一名45岁无症状淋巴管平滑肌瘤病女性患者，其出现一个大囊肿，看似气胸状态。尽管胸部X线片及后续CT扫描偶然诊断为右侧气胸，但通过引流及电视辅助胸腔镜手术治疗，使我们能够正确诊断LAM中的囊肿。
