Yamagiwa I, Ohta M, Obata K, Washio M
Second Department of Surgery, Yamagata University School of Medicine, Japan.
Z Kinderchir. 1988 Apr;43(2):108-9. doi: 10.1055/s-2008-1043428.
A case report of biliary atresia associated with preduodenal portal vein is presented with a review of 27 similar cases previously reported. The occurrence of associated anomalies in these 28 cases has a much higher frequency (82%) than coincidental association. They were associated with cardiovascular anomalies in 71%, polysplenia in 68%, malrotation of the intestine in 61%, situs inversus in 22% and duodenal atresia in 9%. Developmental anomaly is considered to participate strongly in the aetiology of biliary atresia combined with preduodenal portal vein.
本文报告一例十二指肠前门静脉伴发胆道闭锁的病例，并回顾了此前报道的27例类似病例。这28例中相关异常的发生率（82%）远高于偶然关联。其中71%伴有心血管异常，68%伴有多脾，61%伴有肠旋转不良，22%伴有内脏反位，9%伴有十二指肠闭锁。发育异常被认为在十二指肠前门静脉合并胆道闭锁的病因中起重要作用。
