Department of Diagnostic Radiology, Clinique St Luc, Bouge, 5004, Namur, Belgium.
Surg Radiol Anat. 2021 Sep;43(9):1497-1501. doi: 10.1007/s00276-021-02751-4. Epub 2021 Apr 24.
Meandering right pulmonary vein (MRPV) is an exceedingly rare congenital pulmonary vascular variant with less than 20 reported cases. MPVR is a tortuous aberrant venous drainage of the right pulmonary upper lobe anastomosing with the right lower pulmonary vein instead of directly joining the left atrium. The variant is benign with an orthotopic venous drainage without any kind of shunting. The differential diagnosis mostly comprises the scimitar syndrome but also primary varix, arteriovenous malformations, and pulmonary sequestration. We report a case of MRPV fortuitously diagnosed in a 70-year-old patient. Multi-detector computed tomographic angiography (CTA) with MPR, MIP, and 3D reconstructions allowed the diagnosis obviating the need for invasive procedures.
右肺静脉走行异常(MRPV)是一种极为罕见的先天性肺血管变异,仅有不到 20 例报道。MRPV 是一种右肺上叶的迂曲异常静脉引流,与右下肺静脉吻合,而不是直接汇入左心房。该变异为良性,具有正常的静脉回流,无任何分流。鉴别诊断主要包括弯刀综合征,但也包括原发性静脉瘤、动静脉畸形和肺隔离症。我们报告了一例 70 岁偶然诊断的 MRPV 患者。多排螺旋 CT 血管造影(CTA)联合 MPR、MIP 和 3D 重建可以明确诊断,避免了有创性操作。