Michaud Pierre-Luc, Gebril Mohamed
Department of Dental Clinical Sciences, Faculty of Dentistry, Dalhousie University, Halifax, Nova Scotia, Canada.
Am J Case Rep. 2021 Apr 26;22:e929816. doi: 10.12659/AJCR.929816.
BACKGROUND Eagle syndrome is an unusual condition in which the styloid process (SP) becomes elongated and causes different clinical symptoms due to pressure on adjacent anatomical structures. The symptoms are non-specific and include severe throat, facial, and ear pain, or headaches. They are usually exacerbated by head rotation, swallowing, yawning, or chewing, but atypical presentations exist. It is a difficult pathology to diagnose and it can take several years before a proper diagnosis is made. CASE REPORT This report describes the case of a dental student presenting with an atypical presentation of Eagle syndrome. His styloid processes were 75 mm long and he was affected with severe pain to his throat, the anterior part of his ears, his submandibular area, and his molar teeth. The pain was exacerbated during maximal mouth opening, yawning, mandibular protrusion, and during downward head tilt, but not during the classically described movements of head rotation, swallowing, yawning, or chewing. Due to the absence of the classic symptoms, even with knowledge of the condition and unusual direct access to several oral and maxillofacial specialists, it took 4 years and multiple misdiagnoses to reach the final diagnosis. Following bilateral styloidectomy, all pain subsided. CONCLUSIONS The clinical presentation of Eagle syndrome varies, and the symptoms are non-specific. This greatly increases the complexity of diagnosing the condition and raises the time to diagnosis and the chances of misdiagnoses. It is, therefore, crucial to recognize the diagnostic tools, applicable imaging, and definitive treatment alternatives to successfully identify and treat patients affected.
鹰综合征是一种罕见病症,其中茎突(SP)变长并因对相邻解剖结构的压迫而导致不同的临床症状。症状不具有特异性,包括严重的咽喉、面部和耳部疼痛或头痛。这些症状通常在头部旋转、吞咽、打哈欠或咀嚼时加重,但也存在非典型表现。这是一种难以诊断的病理状况,可能需要数年才能做出正确诊断。病例报告:本报告描述了一名牙科学生出现鹰综合征非典型表现的病例。他的茎突长75毫米,喉咙、耳前部、下颌下区域和磨牙严重疼痛。在最大程度张口、打哈欠、下颌前突和头部向下倾斜时疼痛加剧,但在经典描述的头部旋转、吞咽、打哈欠或咀嚼动作时疼痛不加剧。由于缺乏典型症状,即使了解该病症且能直接接触到多位口腔颌面专家,最终诊断也花费了4年时间且出现多次误诊。双侧茎突切除术后,所有疼痛均消失。结论:鹰综合征的临床表现各异,症状不具有特异性。这大大增加了诊断该病症的复杂性,延长了诊断时间并增加了误诊几率。因此,认识诊断工具、适用的影像学检查和明确的治疗方案对于成功识别和治疗受影响患者至关重要。