Bouardi Nizar El, Lamrani Moulay Youssef Alaoui, Haloua Meriam, Alami Badrredine, Boubou Meryem, Maaroufi Mustapha
Service de Radiologie, Centre Hospitalier Universitaire Hassan II, Fès, Maroc.
Faculté de Médecine et de Pharmacie, Université Sidi Mohammed Ben Abdellah, Fès, Maroc.
Pan Afr Med J. 2021 Feb 8;38:136. doi: 10.11604/pamj.2021.38.136.28043. eCollection 2021.
Sclerosing encapsulating peritonitis is a very rare pathological entity. It is a chronic fibroinflammatory disease affecting the peritoneum and leading to the formation of diffuse egg-shell-shaped fibrous capsule which totally or locally encapsulate the abdominal viscera, in particular the digestive tract. Clinical signs are little specific and misleading. Medical imaging, including computed tomography, can help clinicians to make a diagnosis, by highlighting a thin peritoneal membrane encompassing an agglutination of digestive loops. Secondary types (postperitoneal dialysis, tuberculosis, medications, postintraperitoneal chemotherapy) are quite common, however idiopathic sclerosing encapsulating peritonitis is very rare and few cases have been reported in the literature. We here report the case of a 53-year-old woman with idiopathic sclerosing encapsulating peritonitis.
硬化性包裹性腹膜炎是一种非常罕见的病理实体。它是一种慢性纤维炎症性疾病,影响腹膜并导致形成弥漫性蛋壳样纤维性包膜,该包膜完全或局部包裹腹腔脏器,尤其是消化道。临床症状特异性不强且具有误导性。包括计算机断层扫描在内的医学影像检查,通过凸显围绕消化袢粘连的薄腹膜,可帮助临床医生做出诊断。继发性类型(腹膜透析后、结核、药物、腹腔内化疗后)较为常见,然而特发性硬化性包裹性腹膜炎非常罕见,文献中报道的病例很少。我们在此报告一例53岁特发性硬化性包裹性腹膜炎女性患者的病例。