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抗磷脂抗体阳性女性的红细胞增多症与栓塞:一项诊断挑战。

Erythrocytosis, embolism in a woman with antiphospholipid antibodies: A diagnostic challenge.

作者信息

Siddiqa Ayesha, Haider Asim, Mehmood Maham, Hanif Ahmad

机构信息

Department of Internal Medicine BronxCare Health System Bronx NY USA.

Hematology and Oncology BronxCare Health System Bronx NY USA.

出版信息

Clin Case Rep. 2021 Feb 24;9(4):2138-2143. doi: 10.1002/ccr3.3965. eCollection 2021 Apr.

DOI:10.1002/ccr3.3965
PMID:33936653
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC8077322/
Abstract

Systemic thromboembolism, along with acute multiorgan failure, should raise clinical suspicion for CAPS. Timely management, even in suspected cases, can have a significant impact on mortality.

摘要

系统性血栓栓塞,连同急性多器官功能衰竭,应引起临床对灾难性抗磷脂综合征(CAPS)的怀疑。即使在疑似病例中,及时治疗也会对死亡率产生重大影响。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/83cd/8077322/06b16003b003/CCR3-9-2138-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/83cd/8077322/fa1905d00baa/CCR3-9-2138-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/83cd/8077322/d91d7afe5f76/CCR3-9-2138-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/83cd/8077322/06b16003b003/CCR3-9-2138-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/83cd/8077322/fa1905d00baa/CCR3-9-2138-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/83cd/8077322/d91d7afe5f76/CCR3-9-2138-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/83cd/8077322/06b16003b003/CCR3-9-2138-g004.jpg

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本文引用的文献

1
Re-evaluation of hematocrit as a determinant of thrombotic risk in erythrocytosis.重新评估红细胞增多症中血细胞比容作为血栓形成风险的决定因素。
Haematologica. 2019 Apr;104(4):653-658. doi: 10.3324/haematol.2018.210732. Epub 2019 Mar 14.
2
36-year-old female with catastrophic antiphospholipid syndrome treated with eculizumab: a case report and review of literature.36岁女性灾难性抗磷脂综合征患者接受依库珠单抗治疗:病例报告及文献复习
Case Rep Hematol. 2014;2014:704371. doi: 10.1155/2014/704371. Epub 2014 Oct 15.
3
Catastrophic antiphospholipid syndrome: a clinical review.
灾难性抗磷脂综合征:临床综述
J Nephropathol. 2014 Jan;3(1):9-17. doi: 10.12860/jnp.2014.03. Epub 2014 Jan 1.
4
Catastrophic antiphospholipid syndrome with severe acute thrombotic microangiopathy and hemorrhagic complications.伴有严重急性血栓性微血管病和出血并发症的灾难性抗磷脂综合征。
Case Rep Med. 2013;2013:915309. doi: 10.1155/2013/915309. Epub 2013 Dec 9.
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Antiphospholipid syndrome.抗磷脂综合征
Hematology Am Soc Hematol Educ Program. 2013;2013:675-80. doi: 10.1182/asheducation-2013.1.675.
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Catastrophic antiphospholipid syndrome: how to diagnose a rare but highly fatal disease.灾难性抗磷脂综合征:如何诊断一种罕见但致命的疾病。
Ther Adv Musculoskelet Dis. 2013 Dec;5(6):305-14. doi: 10.1177/1759720X13502919.
7
Prevalence of venous thromboembolism in patients with secondary polycythemia.继发性红细胞增多症患者静脉血栓栓塞症的患病率。
Clin Appl Thromb Hemost. 2013 Jul-Aug;19(4):363-6. doi: 10.1177/1076029612460425. Epub 2012 Sep 23.
8
Isolated elevation of IgA anti-beta2glycoprotein I antibodies with manifestations of antiphospholipid syndrome: a case series of five patients.伴有抗磷脂综合征表现的 IgA 抗β2糖蛋白 I 抗体孤立性升高:五例患者的病例系列。
Lupus. 2009 Oct;18(11):1011-4. doi: 10.1177/0961203309103048.
9
Catastrophic antiphospholipid syndrome (CAPS): descriptive analysis of a series of 280 patients from the "CAPS Registry".灾难性抗磷脂综合征(CAPS):来自“CAPS注册研究”的280例患者系列的描述性分析
J Autoimmun. 2009 May-Jun;32(3-4):240-5. doi: 10.1016/j.jaut.2009.02.008. Epub 2009 Mar 26.
10
V meeting of the European forum on antiphospholipid antibodies.
Autoimmun Rev. 2006 Aug;5(7):499-507. doi: 10.1016/j.autrev.2006.01.001. Epub 2006 Feb 3.