Institute of Heart, Lung and Transplantation, Gleneagles Global Health City, Chennai, Tamil Nadu, India.
Ann Card Anaesth. 2021 Jan-Mar;24(1):79-82. doi: 10.4103/aca.ACA_165_19.
Pulmonary Alveolar Microlithiasis (PAM) is a rare autosomal recessive end stage lung condition characterized by widespread alveolar deposition of calcium microliths. It is worth emphasis india has reported 80 cases out of 1022 cases worldwide but there is no report on lung transplant and and anaesthetic management in this category of patient. This report present the anaesthetic challenge in management of first indian patient with the diagnosis of PAM, who underwent bilateral lung transplantation. Bilateral lung transplantation is one of the most challenging surgeries that require the care of a cardiothoracic anesthesiologist. Utilization of extracorporeal circulation has allowed a safer performance of this procedure in patients with severe cardiopulmonary compromise. Intraoperative management is a pivotal part of the patient's care, as it contributes to the patient's overall outcome.
肺肺泡微结石症（PAM）是一种罕见的常染色体隐性终末期肺部疾病，其特征是广泛的肺泡钙微结石沉积。值得强调的是，印度在全球 1022 例病例中报告了 80 例，但在这一类别患者的肺移植和麻醉管理方面没有报告。本报告介绍了首例印度 PAM 患者的麻醉管理挑战，该患者接受了双侧肺移植。双侧肺移植是最具挑战性的手术之一，需要心胸麻醉师的护理。体外循环的使用使严重心肺功能障碍患者更安全地进行了该手术。术中管理是患者护理的关键部分，因为它有助于患者的整体预后。
