From the Department of Anesthesiology, The University of Iowa, Iowa City, Iowa.
A A Pract. 2021 May 4;15(5):e01461. doi: 10.1213/XAA.0000000000001461.
Goldenhar syndrome, or oculoauriculovertebral dysplasia, represents approximately 10% of craniofacial microsomia anomalies. These patients have a variety of clinical features that are relevant to anesthesia providers, including a high-arched palate, mandibular hypoplasia, micrognathia, and temporomandibular joint (TMJ) malformation. The oral manifestations of Goldenhar syndrome range from malocclusion to complex TMJ involvement. Outside of the dental and oral surgery literature, the potential for TMJ ankylosis in Goldenhar patients is seldom emphasized. TMJ ankylosis impacts airway management, and anesthesia providers must be aware of this clinical phenotype when planning the anesthetic care of patients with Goldenhar syndrome.
Goldenhar 综合征，又称眼-耳-脊椎发育不良，占颅面骨发育不全畸形的 10%左右。这些患者有多种与麻醉提供者相关的临床特征，包括高拱形腭、下颌骨发育不全、小颌畸形和颞下颌关节（TMJ）畸形。Goldenhar 综合征的口腔表现从咬合不正到复杂的 TMJ 受累不等。在牙科和口腔外科学文献之外，Goldenhar 患者 TMJ 强直的可能性很少被强调。TMJ 强直影响气道管理，麻醉提供者在为 Goldenhar 综合征患者制定麻醉护理计划时必须意识到这种临床表型。
