Department of Pediatrics, Yale School of Medicine, Yale University, New Haven, CT, USA.
Department of Genetics, Yale School of Medicine, Yale University, New Haven, CT, USA.
FASEB J. 2021 Jun;35(6):e21627. doi: 10.1096/fj.202002783RR.
Capillary endothelial cells (ECs) maintain a semi-permeable barrier between the blood and tissue by forming inter-EC tight junctions (TJs), regulating selective transport of fluid and solutes. Overwhelming inflammation, as occurs in sepsis, disrupts these TJs, leading to leakage of fluid, proteins, and small molecules into the tissues. Mechanistically, disruption of capillary barrier function is mediated by small Rho-GTPases, such as RhoA, -B, and -C, which are activated by guanine nucleotide exchange factors (GEFs) and disrupted by GTPase-activating factors (GAPs). We previously reported that a mutation in a specific RhoB GAP (p190BRhoGAP) underlays a hereditary capillary leak syndrome. Tumor necrosis factor (TNF) treatment disrupts TJs in cultured human microvascular ECs, a model of capillary leak. This response requires new gene transcription and involves increased RhoB activation. However, the specific GEF that activates RhoB in capillary ECs remains unknown. Transcriptional profiling of cultured tight junction-forming human dermal microvascular endothelial cells (HDMECs) revealed that 17 GEFs were significantly induced by TNF. The function of each candidate GEF was assessed by short interfering RNA depletion and trans-endothelial electrical resistance screening. Knockown of ArhGEF10 reduced the TNF-induced loss of barrier which was phenocopied by RhoB or dual ArhGEF10/RhoB knockdown. ArhGEF10 knockdown also reduced the extent of TNF-induced RhoB activation and disruption at tight junctions. In a cell-free assay, immunoisolated ArhGEF10 selectively catalyzed nucleotide exchange to activate RhoB, but not RhoA or RhoC. We conclude ArhGEF10 is a TNF-induced RhoB-selective GEF that mediates TJ disruption and barrier loss in human capillary endothelial cells.
毛细血管内皮细胞 (ECs) 通过形成细胞间紧密连接 (TJs) 来维持血液和组织之间的半透性屏障,调节液体和溶质的选择性运输。在败血症等炎症反应中,过度的炎症会破坏这些 TJ,导致液体、蛋白质和小分子渗漏到组织中。从机制上讲,毛细血管屏障功能的破坏是由小 Rho-GTPases 介导的,如 RhoA、-B 和 -C,它们被鸟嘌呤核苷酸交换因子 (GEFs) 激活,并被 GTPase 激活因子 (GAPs) 破坏。我们之前报道过,一种特定的 RhoB GAP(p190BRhoGAP)突变是遗传性毛细血管渗漏综合征的基础。肿瘤坏死因子 (TNF) 处理破坏了培养的人微血管内皮细胞 (HDMECs) 中的 TJ,这是毛细血管渗漏的模型。这种反应需要新的基因转录,并涉及 RhoB 激活增加。然而,激活毛细血管 ECs 中 RhoB 的特定 GEF 仍然未知。培养的紧密连接形成的人类皮肤微血管内皮细胞 (HDMECs) 的转录谱分析显示,17 种 GEFs 被 TNF 显著诱导。通过短干扰 RNA 耗竭和跨内皮电阻筛选评估了每个候选 GEF 的功能。ArhGEF10 的敲低减少了 TNF 诱导的屏障丧失,这与 RhoB 或双重 ArhGEF10/RhoB 敲低的表型相似。ArhGEF10 敲低还减少了 TNF 诱导的 RhoB 激活和 TJ 破坏的程度。在无细胞测定中,免疫分离的 ArhGEF10 选择性地催化核苷酸交换以激活 RhoB,但不激活 RhoA 或 RhoC。我们得出结论,ArhGEF10 是一种 TNF 诱导的 RhoB 选择性 GEF,它介导了人毛细血管内皮细胞中 TJ 的破坏和屏障的丧失。