Meredith J T, Cerezo L, Alvarez M, Price G, Bourgeois S
Department of Pathology, Orlando Regional Medical Center, FL 32806.
Arch Pathol Lab Med. 1988 Aug;112(8):833-7.
An unusual case of a progressive, noninflammatory stenosing vasculopathy, arterial fibromuscular dysplasia is presented. The distinctive features of this particular case include onset in early childhood with a predominant involvement of the gastrointestinal system, sparing of the renal arteries, lack of hypertension, and no cutaneous features of progressive systemic sclerosis. We discuss the clinical history over a decade and the pathologic features, including routine and electron microscopic findings of biopsy and autopsy tissues, and review the literature.
