Division of Pediatric Neurosurgery, Hospital de Pediatría Juan P. Garrahan, Combate de los Pozos 1881, 1245, Buenos Aires, ZC, Argentina.
Division of Interventional Neuroradiology, Hospital de Pediatría Juan P. Garrahan, Buenos Aires, Argentina.
Childs Nerv Syst. 2022 Apr;38(4):789-794. doi: 10.1007/s00381-021-05181-0. Epub 2021 May 6.
Cerebral proliferative angiopathy (CPA) is an infrequent vascular malformation. It is composed of a nidus, arterial feeders, and venous drainage. Some special features differentiate it from the common arteriovenous malformations (AVM). The nidus has normal cerebral tissue intermingled and occupies a large portion of the brain. There is a frequent transdural arterial supply. Arterial feeders and draining veins are of small caliber concerning the nidus size. Ischemic strokes are the most common clinical event. Intracranial bleeding when occurs has a worse prognosis due to its high recurrence rate. We have presented two cases of CPA in pediatric patients who required surgical resolution of their acute episode.
脑增殖性血管病(CPA)是一种不常见的血管畸形。它由病灶、动脉供血和静脉引流组成。一些特殊的特征将其与常见的动静脉畸形(AVM)区分开来。病灶由正常脑组织混合而成,占据大脑的很大一部分。存在频繁的硬脑膜动脉供血。动脉供血和引流静脉的口径相对于病灶大小较小。缺血性中风是最常见的临床事件。颅内出血的预后较差,因为其复发率较高。我们介绍了两名儿科患者的 CPA 病例,他们需要手术解决其急性发作。