Department of Dermatology, Escuela de Medicina, Pontificia Universidad Católica de Chile, Santiago, Chile.
Dermatology Service, Department of Medicine, Memorial Sloan Kettering Cancer Center, New York, NY, USA.
Australas J Dermatol. 2021 Aug;62(3):386-389. doi: 10.1111/ajd.13617. Epub 2021 May 11.
Bilateral diffuse uveal melanocytic proliferation (B-DUMP) is a rare paraneoplastic syndrome typically presenting with bilateral visual loss. B-DUMP is associated with extraocular systemic malignancies with the most common being lung cancer in males and uro-gynaecological cancer in females (mainly ovarian cancer). Cutaneous and/or mucosal involvement in patients with B-DUMP has been reported but it is not well characterised. Herein, we present a female in her 70s with diagnosis of stage IV vaginal clear-cell carcinoma and metastatic melanoma of unknown primary that developed progressive bilateral loss of visual acuity compatible with 'B-DUMP'. Simultaneously, she developed multifocal bilateral bluish-greyish patches on the skin that were shown to have a proliferation of dermal melanocytes. We propose that the clinical and histopathologic cutaneous findings seen in patients with B-DUMP be termed 'diffuse integumentary melanocytic proliferation (DIMP)'.
双侧弥漫性葡萄膜黑色素细胞增生症(B-DUMP)是一种罕见的副肿瘤综合征,典型表现为双侧视力丧失。B-DUMP 与眼外全身恶性肿瘤有关,最常见于男性的肺癌和女性的泌尿生殖系统癌症(主要是卵巢癌)。已有报道称 B-DUMP 患者存在皮肤和/或黏膜受累,但特征描述不详。在此,我们报告了一名 70 多岁的女性,诊断为 IV 期阴道透明细胞癌和不明原发灶的转移性黑色素瘤,出现进行性双侧视力丧失,符合“B-DUMP”表现。同时,她的皮肤出现多发性双侧蓝灰色斑块,组织病理学显示真皮黑色素细胞增生。我们提出,将 B-DUMP 患者的临床和组织病理学皮肤表现称为“弥漫性皮肤黑色素细胞增生症(DIMP)”。