心内膜心肌纤维化中肺动脉瓣过早开放。

Premature opening of the pulmonary valve in endomyocardial fibrosis.

作者信息

Okamoto M, Amioka H, Hashimoto M, Shimamoto H, Sakura E, Yokote Y, Yamagata T, Tsuchioka Y, Matsuura H, Kajiyama G

机构信息

First Department of Internal Medicine, Hiroshima University School of Medicine, Japan.

出版信息

Jpn Heart J. 1988 Jan;29(1):127-33. doi: 10.1536/ihj.29.127.

DOI:10.1536/ihj.29.127

PMID:3398241

Abstract

Two-dimensional and Doppler echocardiographic findings in a 67-year-old man with endomyocardial fibrosis (EMF) are described. The two-dimensional echocardiogram showed typical features of EMF, right ventricular endomyocardial calcification, a thickened right ventricular wall, obliteration of the apex of the right ventricle and marked dilatation of the right atrium. In addition, premature opening of the pulmonary valve was observed during late diastole. The Doppler echocardiogram revealed forward flow from the right ventricle to the pulmonary artery, indicating the conduit state of the right ventricle. These findings were supported by cardiac catheterization and autopsy. Thus, two-dimensional and Doppler echocardiography are useful not only in making the diagnosis, but also in understanding the hemodynamic condition in EMF.

摘要

描述了一名67岁患有心内膜心肌纤维化（EMF）男性的二维和多普勒超声心动图检查结果。二维超声心动图显示了EMF的典型特征，右心室心内膜钙化、右心室壁增厚、右心室心尖闭塞以及右心房明显扩张。此外，在舒张晚期观察到肺动脉瓣提前开放。多普勒超声心动图显示有从右心室到肺动脉的前向血流，提示右心室的管道状态。这些发现得到了心导管检查和尸检的证实。因此，二维和多普勒超声心动图不仅有助于诊断，还能帮助了解EMF中的血流动力学状况。