The University of Texas Medical Branch, Galveston, TX, USA.
UCLA-Kern Medical, Bakersfield, CA, USA.
J Investig Med High Impact Case Rep. 2021 Jan-Dec;9:23247096211014690. doi: 10.1177/23247096211014690.
Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome is a sexual developmental disorder. In this disorder, there is a congenital absence of the uterus and vagina with normal external genitalia. The etiology is not well understood. Variations of this condition exist that may include congenital abnormalities and psychological problems. In this article, we discuss the case of a 47-year-old African American female who presented with acute renal failure, solitary right kidney, and a pelvic mass extending from the pelvis to the right hypochondrium determined to be a fibroid. The patient was managed by a multidisciplinary team, dialyzed, and planned for removal of the mass. While understanding the low probability of having fibroids without a uterus, fibroids should not be excluded from such patients. It is also important to consider the emotional and psychological well-being of such patients.
梅耶尔-罗基坦斯基-库斯特-豪泽（MRKH）综合征是一种性发育障碍。在这种疾病中，子宫和阴道先天缺失，而外生殖器正常。其病因尚不清楚。这种情况存在多种变异，可能包括先天性异常和心理问题。本文讨论了一位 47 岁的非裔美国女性的病例，她表现为急性肾衰竭、孤立的右肾和从骨盆延伸到右季肋部的盆腔肿块，被诊断为子宫肌瘤。该患者由多学科团队管理，进行了透析，并计划切除肿块。尽管了解到没有子宫的情况下子宫肌瘤的可能性较低，但仍不应排除此类患者的子宫肌瘤。考虑到此类患者的情绪和心理健康也很重要。
