Mourad Ali P, De Robles Marie Shella, Winn Robert Dr
Department of Surgery, The Wollongong Hospital, Wollongong, NSW 2500, Australia.
SAGE Open Med Case Rep. 2021 Apr 29;9:2050313X211009717. doi: 10.1177/2050313X211009717. eCollection 2021.
Behcet's syndrome is a systemic inflammatory disorder that involves several organ systems and is exceptionally rare in the Western world. The diagnosis is frequently difficult as it resembles several other disease processes. A 23-year-old male with a previous presumptive diagnosis of Crohn's disease presented to our unit with genital ulceration. This is on a background of recurrent perianal abscesses requiring surgical drainage and seton placement. He subsequently developed a complex perianal fistula extending from the rectum to the perineum and left groin. After drainage and an unsuccessful trial of biologic immunosuppressive therapy, he developed several papulopustular cutaneous lesions and oral ulcerations. The diagnostic criteria for Behcet's syndrome was met and he was referred to a rheumatologist for ongoing management.
白塞病是一种累及多个器官系统的全身性炎症性疾病，在西方世界极为罕见。由于其与其他几种疾病过程相似，诊断常常困难。一名先前被推定诊断为克罗恩病的23岁男性因生殖器溃疡前来我院就诊。其背景是反复出现肛周脓肿，需要手术引流和放置挂线。随后，他出现了一个复杂的肛周瘘管，从直肠延伸至会阴和左腹股沟。在引流及生物免疫抑制治疗试验失败后，他出现了多处丘疹脓疱性皮肤病变和口腔溃疡。符合白塞病的诊断标准，他被转诊给风湿病学家进行持续治疗。
