Mohamed Ahmed Osama, Eradi Bala, Owen Anthony, Rajimwale Ashok
Department of Paediatric Surgery, Leicester Royal Infirmary, Infirmary Square, leicester, LE1 5WW, UK.
Case Rep Urol. 2021 Apr 26;2021:6647692. doi: 10.1155/2021/6647692. eCollection 2021.
Posterior urethral valves are a common cause of congenital bladder outlet obstruction. Known associations include cardiac malformations and gastrointestinal abnormalities. In this case series, we report on two cases of PUV associated with anorectal malformations along with a case of PUV in monochorionic diamniotic twins. We explore the difficulty in achieving a diagnosis and the final management. The association of posterior urethral valves in a patient with anorectal malformation should be suspected in case of associated oligohydramnios or oliguria postnatally. There should be a high index of suspicion in twin pregnancy even if only one of the twins is suspected of bladder outlet obstruction.
后尿道瓣膜是先天性膀胱出口梗阻的常见原因。已知的相关病症包括心脏畸形和胃肠道异常。在本病例系列中，我们报告了两例后尿道瓣膜合并肛门直肠畸形的病例以及一例单绒毛膜双羊膜囊双胎中的后尿道瓣膜病例。我们探讨了诊断的困难以及最终的治疗方法。对于出生后伴有羊水过少或少尿的患者，应怀疑存在后尿道瓣膜合并肛门直肠畸形。即使在双胎妊娠中仅怀疑其中一个胎儿存在膀胱出口梗阻，也应高度怀疑。
