Ulcerative ileojejunitis associated with pulmonary fibrosis and polymyositis.

Ulcerative ileojejunitis is a rare condition. We describe a patient who developed this on a background of longstanding celiac disease. Long-term remission has been maintained on corticosteroids. Recently polymyositis and an inflammatory alveolitis have developed, both responding to a higher dose of prednisolone. Relationships between celiac disease and ulcerative ileojejunitis, polymyositis and fibrosing alveolitis have been previously described, and it is of interest that an auto-immune pathophysiology has been implicated in each of these conditions.