视网膜 Racemose 血管瘤（视网膜动静脉交通）的诊断与多模态成像管理。
RETINAL RACEMOSE HEMANGIOMA (RETINAL ARTERIOVENOUS COMMUNICATION) DIAGNOSED AND MANAGED WITH MULTIMODAL IMAGING.
机构信息
Vitreous Retina Macula Consultants of New York, New York, New York.
Columbia University College of Physicians and Surgeons, New York, New York.
出版信息
Retin Cases Brief Rep. 2023 May 1;17(3):279-284. doi: 10.1097/ICB.0000000000001167.
BACKGROUND/PURPOSE: Retinal racemose hemangioma is a rare congenital abnormality of the retinal vasculature with a variety of secondary manifestations that can cause vision loss, including macular edema. This report aims to demonstrate the use of swept-source optical coherence tomography angiography in further characterizing this abnormality.
METHODS
Case report with multimodal imaging including swept-source optical coherence tomography angiography.
RESULTS
A 56-year-old woman with blurred vision was diagnosed macular edema secondary to retinal racemose hemangioma. Localization of the arterial-venous connection was identified with swept-source optical coherence tomography angiography at the deep capillary plexus. Conservative management of the associated foveal exudation ultimately led to a favorable outcome.
CONCLUSION
Observation or topical therapy may be useful and warranted in select cases of retinal racemose hemangioma. The anomalous vascular connection in retinal racemose hemangioma seems to originate at the level of the deep capillary plexus in this case; however, larger studies are necessary for corroboration. Evolving angiographic modalities such as swept-source optical coherence tomography angiography may continue to provide insights for this rare disease.
背景/目的：视网膜螺旋状血管瘤是一种罕见的视网膜血管先天异常，具有多种继发性表现，可导致视力丧失，包括黄斑水肿。本报告旨在展示扫频源光相干断层扫描血管造影在进一步描述这种异常中的应用。
方法
病例报告，包括扫频源光相干断层扫描血管造影等多种成像方式。
结果
一名 56 岁女性因视网膜螺旋状血管瘤继发黄斑水肿导致视力模糊。扫频源光相干断层扫描血管造影在深层毛细血管丛中定位到动静脉连接。对相关黄斑部渗出物进行保守治疗，最终结果良好。
结论
在选择的视网膜螺旋状血管瘤病例中，观察或局部治疗可能是有用且合理的。在这种情况下，视网膜螺旋状血管瘤中异常的血管连接似乎起源于深层毛细血管丛；然而，还需要更大的研究来证实这一点。扫频源光相干断层扫描血管造影等新兴血管造影方式可能会继续为这种罕见疾病提供新的见解。
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